Langerhans cell histiocytosis: a rare cause of cholestasis in adult patients. Case report. Histiocitosis de Langerhans: causa infrecuente de colestasis en el. a Unidad Médico-Quirúrgica de Enfermedades Respiratorias. Área de Neumopatías Intersticiales y Ocupacionales. Hospital Universitario Virgen del Rocío. Abstract. GOMEZ, ANA MARÍA et al. Langerhans cell histiocytosis in children. A description of 10 cases. CES Med. [online]. , vol, n.2, pp

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Relapsing nodular lesions in the course of adult pulmonary Langerhans cell histiocytosis. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field.


A biopsy of the lesions showed that these lesions were compatible with Langerhans cell histiocytosis. N Engl J Med,pp. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. The Journal is published both in Spanish and English. Services on Demand Article. In the year has been indexed in the Histtiocitosis, and has become a vehicle for expressing the most current Spanish medicine and modern. Spanish pdf Article in xml format Article references How to cite this article Automatic translation Send this article by e-mail.

A description of 10 cases. Annals of Pediatrics is the Body of Scientific Expression of the Association and is the vehicle through which members communicate.

In the histioocitosis of multi-systemic involvement, the best results seem to be obtained with prednisone and vinblastine for months. Of the 10 patients 5 had risk organ involvement and 1 died in the observation period.

A liver biopsy was performed after ruling out common pathologies.

There are two patterns of involvement: Subscribe to our Newsletter. The goal with the description of this cases series is to highlight the importance and awareness to a timely diagnosis and management of this entity, for a better quality of life and longer survival.


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In the diagnosis by immunohistochemistry identified Langerhans Cell Histiocytosis, the cases were classified as multisystemic -multifocal in 5 patients, unisystemic in 1 patients – unifocal unisystemic in 1 patients -multifocal eosinophilic granuloma in 3 patients.

Blanco 1C. To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior. If you are a member of the AEDV: Langerhans cell histiocytosis was confirmed in both cases with S hiztiocitosis staining.

The disease prognosis and its response to treatment is langsrhans in the single system form, particularly with bone involvement, and much worse in the multi-system form, especially if several risk organs are involved liver, spleen, bone marrow and lung.

CiteScore measures average citations received per document published. Are you a health professional able to prescribe or dispense drugs? It was informed a cholestasis due to long term obstruction of large biliary ducts. The main pathological finding is the presence of an accumulation of Langerhans histiocytes, which have distinctive nuclei features a central “coffee bean” shaped folding, fine chromatin, and oval shaped nuclei that distinguishes them from conventional histiocytes.

Previous article Next article. Show all Show less. Pulmonary Langerhans cell histiocytosis: Are you a health professional able to prescribe or dispense drugs? Solitary congenital self-healing Langerhans cells histiocytosis.

Histiocitosis de células de Langerhans en niños. Descripción de 10 casos

However, a fistula formed, so a partial fail pancreotomy was performed. Subscribe to our Newsletter. However, histiocitoais risk organs are involved, other chemotherapeutics are needed as well 6-mercaptopurine and metotrexate.

Pediatric Blood and Cancer ; 49 5: It was decided to perform a bypass surgery and a hepaticojejunostomy and a gastrojejunostomy were performed. Liver transplantation in an adult with sclerosing cholangitis due to Langerhans histiociotsis histiocytosis. Etxezarraga 2 and M. Histiocytosis; Langerhans cells; Pediatrics.

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Dear Editor, We present a 42 year old man, with a history of central diabetes insipidus since childhood, primary hyperthyroidism with negative antibodies and seizures since early adulthood. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Gastrointestinal involvement in Langerhan cell histiocytosis.

Discussion There are two patterns of involvement: How to cite histiocitosia article. Are you a health professional able to prescribe or dispense drugs? SRJ is a prestige metric based on the idea that not all citations are the same.

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The Spanish Association of Pediatrics has as one of its main objectives the dissemination of rigorous and updated scientific information on the different areas of pediatrics. Langerhans cell histiocytosis is a rare disease langerhnas different clinical lwngerhans pathological presentation, is clinically divided into three groups: Subscriber If you already have your login data, please click here.

This form of presentation is rare, and seems to be a variant of congenital self-healing reticulohistiocytosis. Si continua navegando, consideramos que acepta su uso. Translators working for the Journal are in charge of the corresponding translations.

One year before coming to our hospital for the first time, he had presented an episode of acute pancreatitis with pseudocyst formation.

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